报道1例肌紧张特殊面容侏儒综合征(SJS)的麻醉处理。患儿男,8岁,18kg,有先天性腭裂和足内旋畸形。2岁出现关节挛缩,步态异常,走路不稳和进行性近视,时有面肌收缩及眼睑痉挛。身体矮小,拄拐杖仅能走40余米。颈部活动自如,但张口受限。肌电图显示面肌有持续高频信号释放。股骨骺变平断裂。右髋关节半脱位。诊断SJS。拟行软组织松解和髋关节稳固术。术 Reported 1 case of muscle tension special facial dwarf syndrome (SJS) anesthesia. Children male, 8 years old, 18kg, congenital cleft palate and internal rotation deformity. 2-year-old joint contracture occurs, abnormal gait, walking and progressive myopia, facial muscle contraction and sometimes blepharospasm. Short stature, crutches can only go more than 40 meters. Neck movement freely, but the mouth is limited. Electromyography shows that facial muscles have sustained high-frequency signal release. Epiphyseal flattening fracture. Right hip subluxation. Diagnose SJS. Proposed soft tissue release and hip stabilization. Surgery