肺出血肾炎综合征,系罕见的自身免疫性疾病,也称抗肾小球基底膜抗体病。本病以急进性肾功能衰竭合并肺出血为主要表现,病情凶险,生前诊断有一定的困难。本病例经肾穿刺病理证实,现报告如下。患者,男性,28岁。间断性咯血1年,肉眼血尿 Pulmonary hemorrhage nephritis syndrome, a rare autoimmune disease, also known as anti-glomerular basement membrane antibody disease. The disease with acute renal failure combined with pulmonary hemorrhage as the main performance, dangerous condition, prenatal diagnosis have some difficulties. The pathological confirmed by renal biopsy, are as follows. Patient, male, 28 years old. Intermittent hemoptysis 1 year, gross hematuria