朗汉斯细胞组织细胞增生症(Langerhans cell histiocytosis,LCH)是一种少见的,病因未明的,以单核-巨噬细胞系统中朗汉斯细胞异常增生为特征的疾病。可造成局限性或广泛性脏器损害。目前为止文献报道LCH共900余例[1],而单发于生殖系统的LCH为10余例[2]。现报道我院收治的1例累及外阴的朗汉斯细胞组织细胞增生症。1病例介绍 Langerhans cell histiocytosis (Langerhans cell histiocytosis, LCH) is a rare, etiological disease characterized by abnormal proliferation of Langerhans cells in the monocyte-macrophage system. Can cause limitations or a wide range of organ damage. So far, more than 900 cases of LCH have been reported in the literature [1], while more than 10 LCHs have been reported in the reproductive system alone [2]. Is reported in our hospital admitted to a case of genital warts of Langerhans cell histiocytosis. 1 case introduction