三尖瓣闭锁是成人中少见的紫绀型先天性心脏病,而合并动脉干永存更为罕见。最近,我们遇见一例,经二维超声心动图获得诊断。患者女性,39岁,工人,因“紫绀39年,左上腹痛3天”入院。患者出生时即有青紫,曾在其他医院诊断为“法乐氏四联症。”幼年时发育尚可,能照常求学。无蹲踞及脑缺氧发作。尚能胜任轻微劳动,但登二楼后出现心慌、气促。近3天来因左上腹持续疼痛,吸气加重,难以忍受,以“先心并发脾梗塞”收入(?)。体检:体温37℃,脉率80次,呼吸20次,血压130/70,发育正常,呈中央型紫绀,明显杵状指、趾,颈静脉显露并见搏动,心尖搏动位于左锁中线 Tricuspid atresia is a rare cyanotic congenital heart disease in adults, and the common carotid artery is more common. Recently, we met with a case that was diagnosed by two-dimensional echocardiography. Female patient, 39 years old, worker, due to “cyanosis 39 years, left upper abdominal pain 3 days” admission. The patient is bruising at birth and has been diagnosed with tetralogy of Fallot in other hospitals. No squat and brain hypoxia attack. Still capable of minor work, but after the second floor appeared palpitation, shortness of breath. Nearly 3 days because of persistent pain in the left upper quadrant, increased inspiratory, unbearable, “congenital spleen infarction” income (?). Physical examination: body temperature 37 ℃, pulse rate 80 times, breathing 20 times, blood pressure 130/70, normal development, central cyanosis, obviously clubbing, toe, jugular vein revealed and see beating, apex beat in the left lock line