恶性混合性苗勒氏管瘤,由Sternberg 等人于1964年介绍,并对肿瘤的上皮和间质成分的结合及其恶性表现作了精确描述。此瘤首次由weber 在1867年描述一例45岁妇女粘液性恶性子宫肿瘤,含有新旧平滑肌组织和横纹肌组织。自1970年来由Kempson 等人据肿瘤内的肉瘤性成分的起源将它分为异源性和同 Malignant mixed Mullerian tumors, described by Sternberg et al. in 1964, accurately described the combination of tumor epithelial and stroma components and their malignant appearance. This tumor was first described by Weber in 1867 as a 45-year-old woman with a mucinous malignant uterine tumor that contained new and old smooth muscle tissue and striated muscle tissue. Since 1970, Kempson et al. classified it as heterogenous and identical according to the origin of the sarcomatous components of tumors.