临床资料患者,女,22岁。入院前18个月在外院行左肘、臀、左足肿物切除术,术后组织病理学检查提示“神经纤维瘤病”。入我院前1个月于当地医院腹部CT检查提示:左侧腹膜后占位(图1);胸部CT示,左侧胸腔积液,左胸腔内占位性病变(图2)。来我院就诊,查体:全身皮肤散在黄褐色斑,大小不一,无明显凸起。全身多发皮下结节,较大者直径1.5 cm。左中上腹部可扪及约15 cm×10 cm大小肿物,质硬,不易推动。在全身麻醉下行开腹探查、腹腔肿物切除术,左侧开胸探查、胸腔肿物切除术。术中见左下腹膜后肿物11 cm×6 cm×6 cm大小,边界清,分离肿物旁的疏松组织,完整切 Clinical data, female, 22 years old. 18 months before admission in the hospital left elbow, hip, left foot tumor resection, postoperative histopathological examination suggested that “neurofibromatosis.” Into our hospital one month before the local hospital abdominal CT examination tips: left retroperitoneal space (Figure 1); chest CT showed left pleural effusion, left chest space-occupying lesions (Figure 2). To our hospital, physical examination: whole body scattered in brown spots, different sizes, no obvious bulge. Multiple subcutaneous nodules, the larger the diameter of 1.5 cm. Middle left abdomen can palpable about 15 cm × 10 cm size of the tumor, hard, not easy to promote. Under general anesthesia laparotomy, abdominal tumor resection, left thoracotomy, thoracic tumor resection. See intraoperative left lower retroperitoneal tumor size of 11 cm × 6 cm × 6 cm, clear boundary, separation of loose tissue next to the tumor, the complete cut