积水性无脑畸形(Hydranencephaly)又称水脑畸形,是一种较为少见的先天性脑畸形。国外发病率0.05‰～0.2%[1,2]。我院1990年1月—1997年7月共收治11例,并通过图像分析来提高对本病的认识和鉴别诊断。1　材料和方法1.1　一般资料　11例中,男性7例,女性4例。年龄1个月～6岁,平均8 Hydroscopic anencephaly (Hydranencephaly), also known as hydrocephalus, is a relatively rare congenital brain deformity. Foreign morbidity 0.05 ‰ ~ 0.2% [1,2]. Our hospital from January 1990 to July 1997 were treated 11 cases, and through image analysis to improve the understanding of the disease and differential diagnosis. 1 Materials and Methods 1.1 General Information 11 cases, 7 males and 4 females. Aged from 1 month to 6 years old, an average of 8