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慢性炎症性脱髓鞘性多发性神经根神经病(CIDP)的诊断迄今形成了五个标准。Barohn标准构成了基本框架,强调临床表现,有助于及时临床诊断。AAN标准特异性较强,但电生理标准过严,敏感性较低。INCAT标准比AAN特异性更强,主要用于临床研究,采用功能障碍量表作为临床受累的证据。Saperstein标准根据临床必须特点分成多数表现和少数表现,前者同时有近端和远端肢体无力,后者只有远端无力。多数表现的类型对免疫治疗有较好的反应。Nicolas标准包括了更多异常的组合,其敏感性为90％,特异性为97％。
The diagnosis of chronic inflammatory demyelinating polyarteritis neuropathy (CIDP) has so far resulted in five criteria. The Barohn standard forms the basic framework that emphasizes clinical presentation and facilitates timely clinical diagnosis. AAN standard specificity, but electrophysiological standards are too strict, less sensitive. The INCAT standard is more specific than AAN and is primarily used in clinical studies, using the Dysfunction Scale as evidence of clinical involvement. The Saperstein criteria are divided into most and minor manifestations based on the characteristics of clinical need, with the former having both proximal and distal limb weakness, the latter having only distal weakness. The majority of manifestations have a better response to immunotherapy. The Nicolas standard includes more unusual combinations with 90% sensitivity and 97% specificity.