血管外皮瘤和淋巴管外皮瘤均为罕见肿瘤。其中血管外皮瘤约占所有血管肿瘤的1%,而淋巴管外皮瘤更为罕见。1942年Staut等首先报告了血管外皮瘤,其后又有很多文章谈到了凡是血管经过的地方都可能出现这种肿瘤。 1955年Enterline等首次报道了淋巴管外皮瘤。1966年Cornog指出,淋巴管肌瘤应作为淋巴管外皮瘤的同义词。作者报道了二例恶性血管外皮瘤。一例为2岁患有多发性血管外皮瘤的女孩。另一例为29岁男性,系 Hemangiopericytoma and lymphangioendothelioma are rare tumors. Among them, hemangiopericytoma accounts for about 1% of all vascular tumors, while lymphangioendothelioma is more rare. In 1942, Staut et al. First reported hemangiopericytoma. Since then, there have been many articles on the possible occurrence of this tumor in any vascular passage. Enterline et al. First reported lymphangiogenesis in 1955. Cornog in 1966 pointed out that lymphangiogenesis should be synonymous with lymphangiogenesis. The authors reported two cases of malignant hemangiopericytoma. An example is a 2 year old girl with multiple hemangiopericytoma. Another example is a 29 year old male, Department