主动脉—肺动脉间隔缺损(简称APF)为一罕见先天畸形,现报告经手术证实为APF二例如下: 例1 女,20岁。因“活动后紫绀15年”于1991年10月16日入院。查体:胸骨左缘第3、4肋问闻及Ⅳ级收缩期吹风性杂音,P_2亢进;周围血管征阳性。胸部X线片:肺血增多,双室增大,右下肺动脉增粗,远侧稍细,主动脉结正常。二维超声心动图:双房、室扩大,肺动脉内径增宽,室间隔未见室水平。多普勒提示室间隔缺损,于主肺动脉内探及肺血增多及肺动脉高压频谱。ECG:窦性心律,右室肥厚伴不完全性右束支传导阻 Aortic - pulmonary septal defect (referred to as APF) is a rare congenital anomalies, are reported to be confirmed by surgery for the following two cases: APF 1 female, 20 years old. Because of “activity cyanosis 15 years” on October 16, 1991 admission. Physical examination: the left sternal third rib 3,4 rib smell and grade IV systolic hair blowing noise, P 2 hyperthyroidism; peripheral vascular signs were positive. Chest X-ray: increased lung blood, double room increases, the lower right pulmonary artery thickening, slightly distal, aortic normal. Two-dimensional echocardiography: double room, room expansion, pulmonary artery diameter widening, no ventricular septal level. Doppler prompted ventricular septal defect, exploration in the main pulmonary artery and increased pulmonary blood and pulmonary hypertension spectrum. ECG: sinus rhythm, right ventricular hypertrophy with incomplete right bundle branch resistance