腺样囊性癌(adenoid cystic carcinoma,ACC)首先在涎腺肿瘤诊断中使用这一名称,后来在乳腺肿瘤诊断中也使用了腺样囊性癌这一名称。之后,在肺、支气管、消化道、皮肤、泪腺、外耳道、前列腺及女性生殖道等器官陆续有腺样囊性癌的报道。食管的腺样囊性癌较少见,本文报道2例发生于食管的腺样囊性癌,并结合文献分析其临床病理学特征,免疫 Adenoid cystic carcinoma (ACC) was first used in the diagnosis of salivary gland tumors, and later in the diagnosis of breast tumors also used the name adenoid cystic carcinoma. Later, lung, bronchial, digestive tract, skin, lacrimal gland, external auditory canal, prostate and female genital tract and other organs have successively reported adenoid cystic carcinoma. Esophageal adenoid cystic carcinoma is rare, this article reports 2 cases of esophageal adenoid cystic carcinoma, and combined with the literature to analyze its clinical and pathological features, immunity