１引言遗传性周围神经病系由于遗传物质变异而出现周围神经病变的一组疾病，可侵犯脑神经及脊神经，其中脊神经病变较常见。大部分是潜隐性起病，进展缓馒，病程可达数年或数十年。症状、体征较对称，多数下肢重于上肢，远端重于近端。有的重点损害不同的神经纤维，如主要损害 1 Introduction Hereditary peripheral neuropathy Department of peripheral neuropathy as a result of genetic material variation in a group of diseases that can invade the cranial nerves and spinal nerves, of which spinal neuropathy is more common. Most of the latent disease, slow progress of bread, the course of up to several years or decades. Symptoms, signs of symmetry, most of the lower limbs are heavier than the upper limbs, distal heavier than the proximal. Some focus damage different nerve fibers, such as major damage