先天性肾上腺皮质增生症是一种常染色体隐性遗传性疾病。临床较少见。1981年～1994年我省儿童医院新生儿病房收治了16例患儿，其中资料较完整的有12例，均为21－羟化酶缺陷失盐型。现分析报道如下。1临床资料1．1一般资料发病年龄4天～20天。男9例，女3例。早产儿1例，足月儿11 Congenital adrenal hyperplasia is an autosomal recessive genetic disease. Clinical less common. From 1981 to 1994, 16 children were admitted to the neonatal ward of Children’s Hospital of our province. Among them, there were 12 cases with complete data, all of which were 21-hydroxylase-deficient-loss-of-salt type. Now analysis reports as follows. 1 Clinical data 1.1 General Information Age of onset 4 days to 20 days. 9 males and 3 females. 1 case of premature children, full-term children 11