报告1例Netherton综合征。患者女,43岁。患者自幼全身皮肤反复出现红斑、脱屑,严重时有渗出,伴有瘙痒。平时头发不易梳理、易断。幼时曾有哮喘史。皮损组织病理改变符合迂回线性鱼鳞病。毛发电镜检查示毛发呈竹节状,在竹节处有套叠。 Report 1 case of Netherton syndrome. Female patient, 43 years old. Patients with systemic erythema repeated since childhood, scaling, severe exudation, accompanied by itching. Usually hair is not easy to comb, easy to break. Have a history of asthma when you were young. Pathological changes in lesions consistent with circuitous linear ichthyosis. Hair microscopy showed hair was bamboo-like, at the bamboo have nested.