先天性无痛无汗症为极少见的疾病 ,我们遇到 2例 ,现报告如下。例 1　女 ,11岁 ,患儿 11个月时 ,夏天烦热 ,自己咬伤手指 ,无疼痛表现 ,去医院就诊 ,诊断为先天性无痛无汗症。患儿智力一般。 10岁时 ,右膝关节外伤 ,活动受限 ,以右膝关节滑膜炎在当地医院行右膝关节滑膜切除术 Congenital painless no sweat disease is a rare disease, we encountered two cases, are as follows. Example 1 female, 11 years old, 11 months with children, irritability in summer, his own bite fingers, no pain performance, go to the hospital for diagnosis of congenital painless no sweat disease. Children with intelligence in general. Right age 10, right knee injury, limited mobility, right knee joint synovitis at the local hospital Right knee synovectomy