房室间隔缺损 (AVSD)既往又称为房室管缺损、房室共同通道或心内膜垫缺损 ,是一较少见的复杂心脏畸形。目前则特指房室瓣结构和功能异常伴房室瓣上下相邻房间隔和室间隔缺损的先天性心脏畸形。Castaneda等提出 ,AVSD无论畸形变异如何 ,应当同时具有下列共同形态学特点 :1房室间 Atrioventricular septal defect (AVSD), formerly known as atrioventricular canal defect, atrioventricular common channel or endocardial cushion defect, is a rare and complex cardiac abnormality. At present, especially refers to atrioventricular valve structure and function abnormalities with atrioventricular valve above and below the adjacent atrial septal defect and congenital heart defects. Castaneda et al. Proposed that regardless of deformity variation, AVSD should have the following common morphological features: 1 AV