患者男性,53岁,农民。右上臂肿块切开引流后出血不止1个多月.于1988年5月13日入院。患者从小起头面部和上肢胸背部有大小不等的皮肤包块,伴有褐色色素沉着。从少年起逐渐驼背,且右上肢比左上肢长、粗。近2年来右上臂肿块由鸽蛋大长大到鸭蛋大,并出现疼痛。1个月前该肿块疼痛明显加重并发热,体温最高39.5℃。当地医院摄x片提示右肱骨骨髓 The patient was male, 53 years old, farmer. The bleeding in the right upper arm was more than 1 month after incision and drainage. He was admitted to hospital on May 13, 1988. The patient started with skin patches of varying sizes on the chest and back of the chest and back, accompanied by brown pigmentation. Gradually hunched from childhood, and the right upper limb is longer and thicker than the left upper limb. In the past 2 years, the right upper arm mass grew from pigeon eggs to large duck eggs and developed pain. One month ago, the pain in the mass was aggravated and he had a fever. His body temperature was highest at 39.5°C. Photographs taken at the local hospital suggest right bone marrow