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(二)视网膜色素变性:我国已有上海、湖南的两大组家系分析,和一些零星报告(合计249家系):部分地区也积累了一些群体患病率资料。群体患病率,据上海、广东、宁夏、河南等地107464人的调查,为0.029％(1∶3467)。遗传方式有常染色体显性,隐性与性连锁隐性三大类。据上海、湖南的大组分析,227个家系中,常染色体隐性最多,常染色体显性与性连锁隐性较少(见表3),与国外相比,最引人注意的是,我国常染色体显性者显然较少,仅占4％(国外为10—40％)。性连锁隐性者也较英美为低,与欧洲大陆较接近。今后,对视网膜
(B) retinitis pigmentosa: China has two major families in Shanghai and Hunan analysis, and some sporadic reports (a total of 249): some areas also accumulated some population prevalence data. The prevalence of the group, according to a survey of 107,464 people in Shanghai, Guangdong, Ningxia, Henan and other places, was 0.029% (1:3467). Genetic methods are autosomal dominant, recessive and sex linked to three major categories of recessive. According to the large group analysis of Shanghai and Hunan, among the 227 pedigrees, autosomal recessiveness is the most common, autosomal dominantness is less associated with sexual intercourse recession (see Table 3), and most notably, compared with foreign countries, China Obviously less autosomal dominant, only 4% (10-40% abroad). Sex-linked recessives are also lower than the Anglo-American, and the closer to the European continent. In the future, on the retina