对１４例肾血管平滑肌脂肪瘤中６例并发出血的患者诊治过程作一小结。复习文献总结国内报道的加本组共１１０例患者，认为国内肾血管平滑肌脂肪瘤有肾外体征的是极少数。Ｂ超，ＣＴ对其诊断及手术方式的选择具有重要意义。出血是一项重要的手术指征，对无症状的小于４ｃｍ直径的肿瘤患者可定期观察。 In 14 cases of renal angiomyolipoma in 6 cases of bleeding complicated by the diagnosis and treatment process to make a summary. Review of the literature summary of the domestic reports plus the group of 110 patients, that the domestic renal artery angiomyolipoma with extrarenal signs are a very small number. B ultrasound, CT of its diagnosis and choice of surgical approach is of great significance. Bleeding is an important indication for surgery and is routinely observed in asymptomatic patients less than 4 cm in diameter.