目的　报告 6例椎管内肠源性囊肿的临床表现、诊断及治疗。方法　分析 6例椎管内肠源性囊肿的病史、临床表现及诊断、治疗情况 ,结合文献加以分析讨论。结果　 6例皆在儿童期发病 ,5例以神经根性疼痛起病 ,6例均有脊髓受压表现 ,2例症状有反复 ,3例有脊柱畸形。 5例手术全切 ,1例大部切除 ,均取得较好疗效。结论　椎管内肠源性囊肿是良性先天性发育异常疾病 ,手术治疗效果好。MIR检查及微创手术的应用是提高诊断和治疗的关键 Objective To report the clinical manifestations, diagnosis and treatment of 6 cases of endogenous intestinal cysts in spinal canal. Methods The history, clinical manifestations, diagnosis and treatment of 6 cases of endogenous intestinal cysts in spinal canal were analyzed and analyzed. Results All the 6 cases were onset in childhood, 5 cases had onset of radicular pain, 6 cases had spinal cord compression, 2 cases had repeated symptoms and 3 cases had spinal deformity. 5 cases of surgical resection, 1 case of most resection, have achieved good effect. Conclusions The intraspinal enterogenous cyst is a benign congenital dysplasia and the surgical treatment is effective. MIR examination and minimally invasive surgery is the key to improving diagnosis and treatment