原发性肝癌（Primary carcinoma of liver PCL)众所周知常并发于酒精性、血色病性、乙型肝炎性或隐原性肝硬化的长期患者，而肝豆状核变性肝硬化并发ＰＣＬ却极为罕见，自 １９５９年迄今，国外文献仅报道 １１例，国内尚未见于文献。我所自１９７８年以来，收治肝豆状核变性住 Primary carcinoma of liver (PCL) is a well-known long-term patient often complicated by alcoholic, hemochromatosis, hepatitis B or cryptogenic cirrhosis. However, it is rare for hepatolenticular cirrhosis complicated by PCL, Since 1959 so far, only 11 cases have been reported in foreign literature, but not yet in the literature in China. Since 1978, I have been living in Wilson’s disease