间叶性软骨肉瘤为罕见的软骨细胞恶性肿瘤 ,而发生于肾脏的间叶性软骨瘤 ,目前国内尚未见报道。我院于 2 0 0 0年 2月收治 1例 ,现报告如下。患者 ,女 ,17岁。因反复右腰部隐痛 8个月 ,血尿 1个月入院。病程中无伴随症状 ,平时可照常上学。体检 :右肾区稍饱满 ,右肾下极可触及 Mesenchymal chondrosarcoma is a rare malignant tumor of cartilage, but occurs in the renal mesenchymal cartilage, at present, has not been reported in China. In our hospital in February 2000 admitted to a case, are as follows. Patient, female, 17 years old. Due to repeated pain in the right lower back 8 months, 1 month hematuria admitted. No symptoms associated with the course of the disease, usually can go to school as usual. Physical examination: a little full right kidney area, the right kidney can reach