一、命名、发病率腺样囊性癌系起源于腺体组织,恶性度较高的肿瘤。通常发生在唾液腺、泪腺、也可在气管、乳腺、皮肤汗腺等处发生。眼眶部泪腺腺样囊性癌是泪腺最常见的恶性肿瘤。在泪腺癌中,腺样囊性癌的发病率是25％和35％。本病最初由Billroth在1859年命名为圆柱瘤,他描述此肿瘤原发于鼻窦,以后穿透到 First, the name, the incidence of adenoid cystic carcinoma originated in the glandular tissue, high-grade tumor. Usually occurs in the salivary glands, lacrimal glands, but also in the trachea, breast, skin sweat glands, etc. occur. Adenoid cystic carcinoma of the lacrimal gland in the eyelid is the most common malignancy of the lacrimal gland. In lacrimal adenocarcinoma, the incidence of adenoid cystic carcinoma is 25% and 35%. The disease was originally named by Billroth in 1859 as a cylindrical tumor. He described this tumor as primary in the sinuses and penetrated later.