遗传性进行性肾炎又称Alport’s综合征,系遗传性家族性疾病。临床主要特点为反复血尿,进行性慢性肾功能衰竭,部分病人合并耳聋及眼病。其肾脏受累的程度与肾外表现频度,在临床上有很大差异。现报道1例如下。患儿,男,14岁。5岁时因背部受剪刀扎伤感染数日后,出现血尿、眼睑浮肿,继之浮肿波及全身。7岁 Hereditary progressive nephritis, also known as Alport’s syndrome, is a hereditary familial disease. Clinical main features of repeated hematuria, progressive chronic renal failure, some patients with deafness and eye disease. The degree of renal involvement and frequency of renal manifestations, there are great clinical differences. 1 case is reported below. Children, male, 14 years old. 5 years old due to the back by scissors wound infection a few days later, hematuria, eyelid edema, followed by edema affected the whole body. 7-year old