骨软骨瘤是一种比较常见的良性肿瘤,有单发性和多发性两种,多发性往往伴有家族史。其遗传方式一般认为是单基因常染色体显性遗传。我们发现一家系,现报告如下。先证者,男,10岁,汉族,玉山县人。患儿因“面色苍黄、间歇性发热”以发热待查收入院。体检中发现左侧7、8前肋,右侧6、7、8前肋上各有一块黄豆大小的硬性肿块,左臂肱骨上端、左腓骨上端和胫骨下端各有一核桃大小肿块,无压 Osteochondroma is a relatively common benign tumor, both single and multiple, often accompanied by multiple family history. The genetic mode is generally considered to be single-gene autosomal dominant. We found a family, the report is as follows. Proof, male, 10 years old, Han nationality, Yushan County. Children because of “pale yellow, intermittent fever” to be admitted to hospital fever check. Physical examination found on the left before the 7,8 ribs, 6,7,8 on the right side of the ribs on the right have a size of hard tumors of soybeans, the left arm, upper humerus, left upper fibular and distal tibia have a walnut-sized lumps, no pressure