原始神经外胚叶肿瘤为罕见的恶性肿瘤,生物学行为高度恶性,易复发、转移、预后差。随着病理检查技术,尤其是免疫组化及细胞遗传学、分子生物学技术的进步,对该病的认识不断提高,报道的病例逐渐增加,现就其相关临床特征进行阐述。1原始神经外胚叶肿瘤的概述原始神经外胚叶肿瘤(P The primitive neuroectodermal tumor is a rare malignant tumor with high malignant biological behavior, easy to recurrence and metastasis, and poor prognosis. With the progress of pathological examination techniques, especially immunohistochemistry and cytogenetics, and molecular biology techniques, the awareness of the disease continues to increase, and the reported cases are gradually increasing. The clinical features of these diseases are now described. A primitive neuroectodermal tumor overview of primitive neuroectodermal tumors (P