血管瘤样“恶性纤维组织细胞瘤(AMFH)”是种分化不确定的中间型肿瘤,大多数发生于年轻人的四肢,具有显著黏液样基质的病例并不常见。作者从一组414例的AMFH中筛选出21例伴有显著黏液样基质的肿瘤(黏液样成分﹥肿瘤成分的60%),分析其临床病理特点及随访情况,部分病例进行荧光原位杂交检测。21例患者女性13例,男性8例,发病年龄2~51岁(中位年龄17岁)。肿瘤位于四肢14 Hemangiomas “Malignant fibrous histiocytoma (AMFH)” is an indefinitely differentiated intermediate tumor, most of which occurs in young people’s limbs. Cases with significant myxoid matrices are uncommon. The authors screened 21 patients with a significant myxoid-like tumor (mucinous sample> 60% of the tumor component) from a panel of 414 AMFHs, analyzed their clinicopathological characteristics and follow-up, and in some cases detected by fluorescence in situ hybridization . Twenty-one patients were female and 13 were female, with 8 males and a mean age of onset of 2 to 51 years (median 17 years). The tumor is located on the extremities 14