鼻腔鼻窦血管肉瘤是来源于血管内皮细胞或向血管内皮细胞分化的间叶细胞的一种非常少见的恶性肿瘤 ,占全部软组织肉瘤的 0 .9% 〔1〕。与其他大多数软组织肉瘤易发生于深层软组织的特点相比 ,血管肉瘤则常发生于头面部、乳腺等皮肤或皮下组织内。尽管鼻腔鼻窦富有血管 ,但发生 Nasal sinuses Angiosarcoma is a very rare malignant tumor of mesenchymal cells derived from vascular endothelial cells or differentiated into vascular endothelial cells, accounting for 0.9% of all soft tissue sarcomas [1]. Compared to most other soft tissue sarcomas, which are prone to deep soft tissue, angiosarcomas often occur in the skin or subcutaneous tissue of the head and face, breast, and the like. Although nasal sinus is rich in blood vessels, it occurs