大龄儿童或成人镰刀综合征常无或仅有轻的临床症状,婴儿则多有严重临床症状和不良预后。作者回顾分析了13例婴儿镰刀综合征,力图明确其严重临床症状的原因。所有病例均经心导管和血管造影证实。首次心导管检查时年龄为1天～6个月;男5例,女8例。13例婴儿均有临床症状,其中11例为严重充血性心力衰竭(8例出现在新生儿期,3例在5个月左右),2例为新生儿期间断性喘鸣或反复咳嗽。13例血管造影均可见右肺静脉全部或部分引流 Older children or adult sickle syndrome often no or only mild clinical symptoms, infants are more serious clinical symptoms and poor prognosis. The authors retrospectively analyzed 13 cases of infantile scythe syndrome in an effort to clarify the causes of their severe clinical symptoms. All cases were confirmed by cardiac catheterization and angiography. The first cardiac catheterization at the age of 1 day to 6 months; 5 males and 8 females. Thirteen infants had clinical symptoms, of which 11 were severe congestive heart failure (8 in the neonatal period and 3 in 5 months), and 2 were intermittent wheezing or recurrent cough during the neonatal period. Thirteen angiography showed all or part of the right pulmonary vein drainage