目的 :进一步了解先天性耳前瘘管的遗传特征。方法 :调查近 16年来收住我院的先天性耳前瘘管 73例 ( 95耳 ) ,对其中 8例作系谱分析。结果 :8例中的双亲之一是同患 ,部分同胞及子女均有可能发病 ,男、女患者均可传给后代 ,全部病例均具有家族同一性 ,可存在隔代遗传现象。结论 :再次肯定先天性耳前瘘管属常染色体显性遗传伴外显不全 Objective: To further understand the genetic characteristics of congenital preauricular fistula. Methods: A total of 73 cases (95 ears) of congenital auricular fistula admitted to our hospital in recent 16 years were investigated. Eight of them were analyzed pedigree. Results: One of the eight parents had the same disease. Some of the siblings and their children were likely to be affected. Both male and female patients could be passed on to offspring. All the cases had familial identity and segregation. CONCLUSIONS: Reaffirming the congenital anterior fistula is an autosomal dominant inheritance with anaphylaxis