先天性外胚叶发育不全缺牙症是一种比较罕见的先天性外胚叶发育异常疾患,具有遗传特征。因为这类病人缺牙的数目和部位差异较大,所以在修复设计时应该灵活掌握。笔者对一例外胚叶发育不全缺牙症的患者,根据缺牙情况,上颌采用覆盖总义齿,下颌采用总义齿修复。临床观察半年表明,义齿在固位和功能恢复方面都取得了比较满意的效果。 Congenital ectodermal hypoplasia Aging is a rare congenital ectodermal dysplasia, with genetic characteristics. Because these patients lack the number and location of large teeth, so the design should be flexible in the repair. The author of a case of ectodermal hypoplastic alveolar patients, according to the situation of missing teeth, covering the maxillary denture, mandibular total denture repair. Six months of clinical observation showed that the denture in the retention and functional recovery have achieved more satisfactory results.