家族性遗传性小脑共济失调一家系１５例报告杨月美张诚钟炎皋先证者Ｖ１，女１０岁，于１９９２年８月１日入院。于１９９１年４月始出现步态不稳，走路易跌，渐出现语言含混不清，进食饮水易呛咳，双手笨拙及意向性震颤，生活尚能自理，智力无下降。查体：行走不稳，步态... Familial hereditary cerebellar ataxia in a family of 15 cases of Yang Yue Mei Zhang Cheng Zhong Yan Gao proband V1, female 10 years old, was admitted on August 1, 1992. At the beginning of April 1991, there was instability in gait, weakness in walking, gradual language ambiguity, easy cough in drinking water, clumsiness in hands and tremor of intention. Life was still able to take care of himself and intelligence did not decline. Physical examination: walking unstable, gait ...