先天性囊性腺瘤样畸形(CCAM)过去认为是一种错构瘤,现在认为是局限性肺发育不良或异常,因囊肿壁可含有骨骼肌【1】,是一种并不少见的先天性肺发育异常。可发生于任何年龄,1岁以内儿童多见。县级医院的误诊率91.67%,皆由于对本病的认识不足误诊,易导致CCAM的新生儿及小婴儿死亡。本文将1例先天性囊性腺瘤样畸形合肺炎心衰的诊断及治疗报告如下。1临床资料:患儿,男,48天,因发现呼吸急促30天,呛奶 Congenital Cystic Adenoma-like Deformity (CCAM), previously considered a hamartoma, is now considered to be localized lung dysplasia or abnormality because the cyst wall may contain skeletal muscle [1], which is not uncommon for congenital Lung dysplasia. Can occur at any age, more common in children under 1 year old. The misdiagnosis rate of county hospitals was 91.67%. All of them were misdiagnosed due to lack of understanding of this disease and could easily lead to the death of newborns and small infants in CCAM. This article will be a case of congenital cystic adenomatoid syndrome pneumonia heart failure diagnosis and treatment are reported as follows. 1 Clinical data: Children, male, 48 days, due to shortness of breath found 30 days, choking milk