先天性肺发育不全,临床极为少见,易误诊为肺不张、肺感染、肺肿瘤等肺部疾病,我们就有关其发病机制、诊断、治疗分析如下。1　病例简介　　患者,男,39岁,因间断咳嗽、咯痰,轻度呼吸困难17年,头晕2h于1999年3月24日入我院呼吸内科。17年前曾由反复发热,左侧胸痛3个月首诊某院内 Congenital lung hypoplasia, clinically rare, easily misdiagnosed as pulmonary atelectasis, pulmonary infection, lung cancer and other lung diseases, we related to its pathogenesis, diagnosis, treatment as follows. 1 Case Profile Patients, male, 39 years old, died of intermittent cough, expectoration, mild dyspnea for 17 years and 2 hours dizzy on March 24, 1999 in our department of respiratory medicine. 17 years ago by the repeated fever, left chest pain for 3 months first visit to a hospital