中枢神经系统肉芽肿性血管炎(Granulomatous angitis of the central nervous system,GACNS)系少见疾病。并发于骨髓增生异常综合征(MDS),未见文献报道。我院于1989年2月收治了1例MDS并GACNS患者,现报告如下。病历摘要张××,女,37岁,已婚,上海籍,工人,住院号251142。患者6岁时因面色苍白,牙龈出血而诊 Central nervous system granulomatous vasculitis (Granulomatous angitis of the central nervous system, GACNS) is a rare disease. Concurrent in myelodysplastic syndrome (MDS), no literature. In our hospital in February 1989 admitted to a case of MDS and GACNS patients, are as follows. Medical record Zhang × ×, female, 37 years old, married, Shanghai nationality, worker, hospital number 251142 Patients at age 6 because of pale, bleeding gums and clinic